Blood coagulation factor XIII and factor XIII deficiency

A Dorgalaleh, J Rashidpanah - Blood reviews, 2016 - Elsevier
Factor XIII (FXIII) is a multifunctional pro-γ-transglutaminase that, in addition to its well-
known role in hemostasis, has a crucial role in angiogenesis, maintenance of pregnancy …

Factor XIII deficiency diagnosis: Challenges and tools

M Karimi, F Peyvandi, M Naderi… - International journal of …, 2018 - Wiley Online Library
Factor XIII deficiency (FXIIID) is a rare hereditary bleeding disorder arising from
heterogeneous mutations, which can lead to life‐threatening hemorrhage. The diagnosis of …

Diagnosis, clinical manifestations and management of rare bleeding disorders in Iran

A Dorgalaleh, SER Alavi, S Tabibian, S Soori… - …, 2017 - Taylor & Francis
ABSTRACT Background: Rare bleeding disorders (RBDs) are heterogeneous disorders,
mostly inherited in an autosomal recessive pattern. Iran is a Mideast country with a high rate …

Intracranial hemorrhage in congenital bleeding disorders

S Tabibian, H Motlagh, M Naderi… - Blood Coagulation & …, 2018 - journals.lww.com
Intracranial hemorrhage (ICH), as a life-threatening bleeding among all kinds of congenital
bleeding disorders (CBDs), is a rare manifestation except in factor XIII (FXIII) deficiency …

Intracranial hemorrhage: a devastating outcome of congenital bleeding disorders—prevalence, diagnosis, and management, with a special focus on congenital factor …

SER Alavi, M Jalalvand, V Assadollahi… - … in thrombosis and …, 2018 - thieme-connect.com
Intracranial hemorrhage (ICH) is a medical emergency. In congenital bleeding disorders,
ICH is a devastating presentation accompanied with a high rate of morbidity and mortality …

Diagnosis of factor XIII deficiency

A Dorgalaleh, S Tabibian, MS Hosseini, Y Farshi… - …, 2016 - Taylor & Francis
Background: Factor XIII (FXIII) deficiency is an extremely rare bleeding disorder with
estimated incidence of one per two million. All routine coagulation tests are normal in FXIII …

The impact of acquired coagulation factor XIII deficiency in traumatic bleeding and wound healing

C Kleber, A Sablotzki, S Casu, M Olivieri, KM Thoms… - Critical Care, 2022 - Springer
Factor XIII (FXIII) is a protein involved in blood clot stabilisation which also plays an
important role in processes including trauma, wound healing, tissue repair, pregnancy, and …

[HTML][HTML] Factor XIII deficiency

A Mangla, H Hamad, RB Killeen, A Kumar - StatPearls [Internet], 2024 - ncbi.nlm.nih.gov
Factor XIII Deficiency - StatPearls - NCBI Bookshelf US flag An official website of the United
States government Here's how you know NIH NLM Logo Access keys NCBI Homepage MyNCBI …

Clinical and laboratory diagnosis of rare coagulation disorders (RCDs)

M Menegatti, R Palla - Thrombosis research, 2020 - Elsevier
Rare coagulation disorders (RCDs) are a group of diseases due to coagulation factors
deficiency leading to life-long bleeding diathesis. The diagnosis of RCDs is challenging due …

Molecular basis of congenital factor XIII deficiency in Iran

A Dorgalaleh, V Assadollahi… - Clinical and applied …, 2018 - journals.sagepub.com
Factor XIII deficiency (FXIIID) is an extremely rare autosomal recessive disorder that has the
highest incidence in Iran. The FXIIID is primarily due to mutations in the FXIII-A gene, most of …