Current understanding and recent developments in common variable immunodeficiency associated autoimmunity

JD Gereige, PJ Maglione - Frontiers in immunology, 2019 - frontiersin.org
Common variable immunodeficiency (CVID) is the most prevalent symptomatic primary
immunodeficiency and comprises a group of disorders with similar antibody deficiency but a …

Lung disease in primary antibody deficiencies

E Schussler, MB Beasley, PJ Maglione - The Journal of Allergy and Clinical …, 2016 - Elsevier
Primary antibody deficiencies (PADs) are the most common form of primary
immunodeficiency and predispose to severe and recurrent pulmonary infections, which can …

International Consensus Document (ICON): common variable immunodeficiency disorders

FA Bonilla, I Barlan, H Chapel… - The journal of …, 2015 - pmc.ncbi.nlm.nih.gov
The International Collaboration in Asthma, Allergy and Immunology initiated an international
coalition among the American Academy of Allergy, Asthma & Immunology; the European …

Autoimmune cytopenias and associated conditions in CVID: a report from the USIDNET registry

EJ Feuille, N Anooshiravani, KE Sullivan… - Journal of clinical …, 2018 - Springer
Purpose Autoimmune cytopenia is frequently a presenting manifestation of common variable
immune deficiency (CVID). Studies characterizing the CVID phenotype associated with …

[HTML][HTML] Endotypes in bronchiectasis: moving towards precision medicine. A narrative review

M Martins, HR Keir, JD Chalmers - Pulmonology, 2023 - Elsevier
Bronchiectasis is a highly complex entity that can be very challenging to investigate and
manage. Patients are diverse in their aetiology, symptoms, risk of complications and …

Primary B-cell immunodeficiencies

T Smith, C Cunningham-Rundles - Human immunology, 2019 - Elsevier
Primary B-cell immunodeficiencies refer to diseases resulting from impaired antibody
production due to either molecular defects intrinsic to B-cells or a failure of interaction …

Granulomatous lymphocytic interstitial lung disease (GLILD) in common variable immunodeficiency (CVID): a multicenter retrospective study of patients from Italian …

F Cinetto, R Scarpa, M Carrabba, D Firinu… - Frontiers in …, 2021 - frontiersin.org
Background: Granulomatous and Lymphocytic Interstitial Lung Diseases (GLILD) is a severe
non-infectious complication of Common Variable Immunodeficiency (CVID), often …

Lung disease in primary antibody deficiency

N Verma, B Grimbacher, JR Hurst - The Lancet Respiratory Medicine, 2015 - thelancet.com
This Review summarises current knowledge on the pulmonary manifestations of primary
antibody deficiency (PAD) syndromes in adults. We describe the major PAD syndromes, with …

Treatment strategies for GLILD in common variable immunodeficiency: a systematic review

OAC Lamers, BM Smits, HL Leavis, GJ de Bree… - Frontiers in …, 2021 - frontiersin.org
Introduction Besides recurrent infections, a proportion of patients with Common Variable
Immunodeficiency Disorders (CVID) may suffer from immune dysregulation such as …

Progression of common variable immunodeficiency interstitial lung disease accompanies distinct pulmonary and laboratory findings

PJ Maglione, JR Overbey… - The Journal of Allergy …, 2015 - Elsevier
Background Common variable immunodeficiency may be complicated by interstitial lung
disease, which leads to worsened morbidity and mortality in some. Although …