Surgical innovation and multidisciplinary management have allowed children born with
univentricular physiology congenital heart disease to survive into adulthood. An estimated …

Over the past decade, as the majority of patients with single ventricle anatomy who have
undergone the Fontan operation reach adulthood, a newly recognized disease process …

2018 AHA/ACC Guideline for the Management of Adults With Congenital Heart Disease: A
Report of the American College of Cardiology/American Heart Association Task Force on …

In 2005, the International Society for Heart and Lung Transplantation (ISHLT) Board of
Directors commissioned the development of the first International Listing Criteria for Heart …

Background: There are limited long-term, single-cohort, follow-up studies available about
patients after the Fontan operation. Objectives: This study sought to determine the long-term …

Aims Liver fibrosis and cirrhosis are a consequence of a Fontan physiology, and determine
prognosis. It is unclear whether non-invasive assessment of liver pathology is helpful to …

We reviewed records of all patients with an initial Fontan operation or revision from 1973 to
2012 at our institution (n= 1,138); 195 patients had postoperative liver data available …

Fontan-associated liver disease (FALD) is a form of congestive hepatopathy that is universal
among patients who have undergone Fontan palliation for functional single ventricle …

Fontan-associated liver disease is a hepatic disorder arising from hemodynamic changes
and systemic venous congestion following Fontan surgery. The histological changes …

Ross et al Transplantation in Congenital Heart Disease 803 listed ACHD patients are more
likely to experience cardiovascular death (including sudden death and death caused by HF) …