Autoimmunity in primary antibody deficiencies

G Azizi, M Ahmadi, H Abolhassani, R Yazdani… - International archives of …, 2017 - karger.com
Primary antibody deficiencies (PADs) are the most common inherited primary
immunodeficiencies in humans, characterized by hypogammaglobulinemia, an inability to …

Agammaglobulinemia: epidemiology, pathogenesis, clinical phenotype, diagnosis, prognosis and management

S Pashangzadeh, R Yazdani, F Nazari… - … Metabolic & Immune …, 2020 - ingentaconnect.com
Agammaglobulinemia is a type of primary antibody deficiencies, characterized by severe
reduction in serum level of all types of immunoglobulins level and absence of B cells in the …

The creation and progress of the J Project in Eastern and Central Europe

L Maródi, J Project Study Group - … of the New York Academy of …, 2011 - Wiley Online Library
Primary immunodeficiencies (PIDs) have now become recognized as a worldwide health
problem. Rapid development of immunological and genetic technologies has led to the …

Анализ клинических проявлений дебюта первичных иммунодефицитов у взрослых

ИА Тузанкина, МЛ Каракина… - Медицинская …, 2014 - cyberleninka.ru
В настоящее время под нашим наблюдением находится 83 взрослых пациента с
различными нозологиями первичных иммунодефицитов. Целью нашей работы было …

Combined Treatment of Progressive Encephalitis in an X-linked Agammaglobulinemia Patient

MA Yamazaki-Nakashimada… - Iranian Journal of …, 2023 - ijaai.tums.ac.ir
Most patients with X-linked agammaglobulinemia are susceptible to infections, while some
cases also suffer from inflammatory or autoimmune complications. We describe a patient …

Progressive neurodegenerative syndrome in a patient with X-linked agammaglobulinemia receiving intravenous immunoglobulin therapy

AT Sag, E Saka, TT Ozgur, O Sanal… - Cognitive and …, 2014 - journals.lww.com
A progressive encephalopathy of unknown etiology has been described in patients with
primary immunodeficiency disorders. In this report, we characterize the clinical features of …

The spread of the J Project

Z Horváth, N Rezaei, I Reisli, I Tuzankina… - Journal of clinical …, 2013 - Springer
The J Project physician education and clinical research collaboration program was
launched in 2004 in Eastern and Central Europe (ECE). In less than 10 years, it has …

Fatal Progressive Meningoencephalitis Diagnosed in Two Members of a Family With X-Linked Agammaglobulinemia

Y Kasahara, M Imamura, C Shin, H Shimizu… - Frontiers in …, 2020 - frontiersin.org
Chronic enteroviral meningoencephalitis is a well-known complication in patients with X-
linked agammaglobulinemia (XLA). However, progressive neurodegenerative disorders or …

Analysis of initial clinical features of primary immunodeficiencies in adults

IA Tuzankina, ML Karakina, EV Vlasova - Medical Immunology (Russia), 2014 - mimmun.ru
At present, we are observing eighty-three adult patients with various primary
immunodeficiencies (PID) of different origin. The aim of our study was to identify the optimal …

Иммунологический статус детей с врожденной агаммаглобулинемией

СО Шарапова, ОЕ Пащенко, АА Мигас… - … навук Беларусі. Серыя …, 2013 - elibrary.ru
Возраст пациента на момент постановки диагноза, врожденная агаммаглобулинемия и
начало заместительной терапии влияют на наличие хронических инфекций верхних и …