Systemic sclerosis

ER Volkmann, K Andréasson, V Smith - The Lancet, 2023 - thelancet.com
Systemic sclerosis, also known as scleroderma, is a rare and complex autoimmune
connective-tissue disease. Once considered an untreatable and unpredictable condition …

Systemic sclerosis–associated interstitial lung disease: How to incorporate two food and drug administration–approved therapies in clinical practice

D Khanna, A Lescoat, D Roofeh… - Arthritis & …, 2022 - Wiley Online Library
Systemic sclerosis (SSc; scleroderma) has the highest individual mortality of all rheumatic
diseases, and interstitial lung disease (ILD) is among the leading causes of SSc‐related …

[HTML][HTML] Diagnosis and management of myositis-associated lung disease

RW Hallowell, SK Danoff - Chest, 2023 - Elsevier
Although interstitial lung disease (ILD) is a leading cause of morbidity and mortality in
patients with inflammatory myopathies, the current definition and diagnostic criteria of …

2023 American College of Rheumatology (ACR)/American College of Chest Physicians (CHEST) guideline for the screening and monitoring of interstitial lung disease …

SR Johnson, EJ Bernstein, MB Bolster… - Arthritis Care & …, 2024 - Wiley Online Library
Objective We provide evidence‐based recommendations regarding screening for interstitial
lung disease (ILD) and the monitoring for ILD progression in people with systemic …

Clinical characteristics, visceral involvement, and mortality in at-risk or early diffuse systemic sclerosis: a longitudinal analysis of an observational prospective …

S Jaafar, A Lescoat, S Huang, J Gordon… - Arthritis research & …, 2021 - Springer
Background Early diffuse cutaneous systemic sclerosis (dcSSc) has the highest case fatality
among rheumatic diseases. We report baseline characteristics, current immunosuppressive …

[PDF][PDF] One year in review 2021: systemic sclerosis

M Di Battista, S Barsotti, M Orlandi, G Lepri… - Clin Exp …, 2021 - clinexprheumatol.org
Systemic sclerosis is a rare and chronic connective tissue disease with a multifaceted
pathogenesis characterised by heterogeneous multi-organ clinical manifestations. Every …

A comprehensive framework for navigating patient care in systemic sclerosis: a global response to the need for improving the practice of diagnostic and preventive …

LA Saketkoo, T Frech, C Varjú, R Domsic… - Best Practice & …, 2021 - Elsevier
Systemic sclerosis (SSc), the most lethal of rheumatologic conditions, is the cause of death
in> 50% of SSc cases, led by pulmonary fibrosis followed by pulmonary hypertension and …

Systemic sclerosis interstitial lung disease: unmet needs and potential solutions

V Liakouli, A Ciancio, F Del Galdo… - Nature Reviews …, 2024 - nature.com
Systemic sclerosis (SSc), or scleroderma, is a rare, complex, systemic autoimmune disease
of unknown aetiology, characterized by high morbidity and mortality often resulting from …

Therapeutic approaches to systemic sclerosis: recent approvals and future candidate therapies

A Lescoat, D Roofeh, M Kuwana, R Lafyatis… - Clinical reviews in …, 2023 - Springer
Systemic sclerosis is the rheumatic disease with the highest individual mortality. The severity
of the disease is determined by the extent of fibrotic changes to cutaneous and internal …

[HTML][HTML] Myositis-associated interstitial lung disease: a comprehensive approach to diagnosis and management

RW Hallowell, JJ Paik - Clinical and experimental rheumatology, 2022 - ncbi.nlm.nih.gov
Interstitial lung disease (ILD) frequently complicates the inflammatory myopathies and at
times is the most prominent clinical feature. Over the years, there has been a growing …