Introduction: The literature of orphan drugs and rare diseases between 2000 and 2014 is
reviewed. The overall structure of its intellectual landscape is characterized in terms of …

Pulmonary arterial hypertension is a serious progressive condition with a poor prognosis if
not identified and treated early. Because the symptoms are nonspecific and the physical …

Aims Pulmonary arterial hypertension (PAH) is a progressive lung disease characterized by
pulmonary vasoconstriction and vascular remodelling, leading to increased pulmonary …

In recent years there has been growing attention to the epistemology of clinical decision‐
making, but most studies have taken the individual physicians as the central object of …

The treatment of pediatric pulmonary arterial hypertension (PAH) is challenging due to the
serious nature of the disease, its rapid progression, and the limited treatment options …

Over the past decade different effective treatment options for use in pulmonary arterial
hypertension (PAH) have been developed. Due to multiple pathophysiological pathways in …

Pulmonary Arterial Hypertension Associated with Adult Congenital Heart Disease, when
Inoperable becomes Operable: A Case Report Page 1 Volume 6 • Issue 3 • 1000350 J Pulm …

This report describes the noncardiac, nonobstetric surgical case of a 29-year old woman
with idiopathic pulmonary arterial hypertension. To safely manage a patient with pulmonary …

Résumé L'hypertension pulmonaire post-embolique (HTPPE) est, par définition, une
hypertension pulmonaire apparaissant dans un contexte d'une maladie thromboembolique …

Pulmonary hypertension (PH) is a complex disorder characterized by an increase in
pulmonary artery pressure ultimately leading to right heart failure. Hypertensive pressures …