Idiopathic pulmonary fibrosis is a type of chronic fibrosing interstitial pneumonia, of unknown
etiology, which is associated with a progressive decrease in pulmonary function and with …

Sarcoidosis is a multisystem inflammatory disorder of unknown cause. It most commonly
affects the pulmonary system but can also affect the musculoskeletal system, albeit less …

Idiopathic pulmonary fibrosis (IPF), the prototype of interstitial lung diseases, has the worst
prognosis and is the only interstitial lung disease for which approved pharmacological …

Background Lymphangioleiomyomatosis (LAM) is included within group 5 of the current PH
classification (unclear multifactorial mechanisms). However, data regarding the occurrence …

Objective Interstitial lung disease (ILD) is highly prevalent in patients with mixed connective
tissue disease (MCTD). However, little is known about the long-term progression of ILD in …

O suporte ventilatório artificial invasivo e não invasivo ao paciente grave tem evoluído e
inúmeras evidências têm surgido, podendo ter impacto na melhora da sobrevida e da …

The use of immunobiological agents for the treatment of autoimmune diseases is increasing
in medical practice. Anti-TNF therapies have been increasingly used in refractory …

Idiopathic pulmonary fibrosis (IPF) is a form of chronic interstitial lung disease of unknown
cause, which predominantly affects elderly men who are current or former smokers. Even …

Idiopathic pulmonary fibrosis (IPF) is a form of chronic fibrosing interstitial pneumonia of
unknown etiology that primarily affects the elderly and for which usual interstitial pneumonia …

OBJECTIVE: To describe the characteristics of a cohort of patients with lung-dominant
connective tissue disease (LD-CTD). METHODS: This was a retrospective study of patients …