A Systematic Review of the Epidemiology and Disease Burden of Congenital and Immune-Mediated Thrombotic Thrombocytopenic Purpura

P Du, T Cristarella, C Goyer, Y Moride - Journal of Blood Medicine, 2024 - Taylor & Francis
Congenital (cTTP) and immune-mediated (iTTP) thrombotic thrombocytopenic purpura are
serious and rare clotting disorders resulting from a deficiency in the ADAMTS13 enzyme. A …

Clinical and laboratory features of patients with acquired thrombotic thrombocytopenic purpura: fourteen years of the Milan TTP registry

I Mancini, S Pontiggia, R Palla, A Artoni… - Thrombosis and …, 2019 - thieme-connect.com
Acquired thrombotic thrombocytopenic purpura (TTP) is a rare thrombotic microangiopathy
caused by the immune-mediated severe deficiency of ADAMTS13. We hereby report the …

Thrombotic thrombocytopenic purpura: a 5‐year tertiary care centre experience

L Swart, E Schapkaitz… - Journal of clinical …, 2019 - Wiley Online Library
Introduction Thrombotic thrombocytopenic purpura (TTP) is associated with high mortality if
not managed timeously with therapeutic plasma exchange (TPE). TTP secondary to human …

The features of acquired thrombotic thrombocytopenic purpura occurring at advanced age

P Agosti, I Mancini, A Artoni, B Ferrari, S Pontiggia… - Thrombosis research, 2020 - Elsevier
Introduction Acquired thrombotic thrombocytopenic purpura (aTTP) is a rare life-threatening
thrombotic microangiopathy (TMA) affecting more frequently women of 30–50 years of age …

Main features of ischemic stroke in patients with acute immune-mediated thrombotic thrombocytopenic purpura

A Truma, I Mancini, P Agosti, A Artoni, JA Giannotta… - Thrombosis …, 2024 - Elsevier
Background Immune-mediated thrombotic thrombocytopenic purpura (iTTP) is a
microangiopathy often characterized by acute neurological involvement including ischemic …

Clinical presentation in thrombotic thrombocytopenic purpura: Real‐world data from two Mexican institutions

E Bugarin‐Estrada, A Gómez‐De León… - Journal of Clinical …, 2018 - Wiley Online Library
Background Thrombotic thrombocytopenic purpura (TTP) is a hematologic disease that can
be fatal if not treated early. We aimed to describe the clinical characteristics of Mexican …

Lombardy diagnostic and therapeutic network of thrombotic microangiopathy

I Mancini, P Agosti, M Boscarino, B Ferrari… - Orphanet Journal of …, 2022 - Springer
Background Thrombotic thrombocytopenic purpura (TTP) is a rare, life-threatening
thrombotic microangiopathy (TMA) requiring urgent treatment. Standardization of its …

Trombotik trombositopenik Purpura Tanılı Hastalarımızın Klinik, Laboratuvar ve Tedavi Sonuçlarının Değerlendirilmesi

S Meşeli, HÜ Teke, N Andıc, E Gunduz - Osmangazi Tıp Dergisi, 2024 - dergipark.org.tr
Thrombotic thrombocytopenic purpura (TTP) is clinically caused by severely deficient activity
of the ADAMTS-13 protease. The classical pentad of TTP, microangiopathic hemolytic …

Trombotik trombositopenik Purpura Tanılı Hastalarımızın Klinik, Laboratuvar ve Tedavi Sonuçlarının Değerlendirilmesi

S MEŞELİ, H ÜSKÜDAR TEKE, N ANDIÇ… - Osmangazi Tıp …, 2024 - avesis.ogu.edu.tr
Trombotik trombositopenik purpura (TTP) klinik olarak ADAMTS-13 proteazının eksik
aktivitesinden kaynaklanır. TTP'nin klasik pentadı mikroanjiyopatik hemolitik anemi (MAHA) …

Clinical presentation, management and outcome of thrombotic thrombocyopenic purpura at the Charlotte Maxeke Johannesburg academic hospital

L Swart - 2019 - wiredspace.wits.ac.za
This is a retrospective study of the clinical and laboratory features, management, and
outcome of 41 adults diagnosed with thrombotic thrombocytopenic purpura (TTP) at the …