The origins of the full-field flash electroretinogram b-wave

Y Bhatt, DM Hunt, LS Carvalho - Frontiers in Molecular Neuroscience, 2023 - frontiersin.org
The electroretinogram (ERG) measures the electrical activity of retinal neurons and glial
cells in response to a light stimulus. Amongst other techniques, clinicians utilize the ERG to …

Early-onset stargardt disease: phenotypic and genotypic characteristics

S Lambertus, RAC van Huet, NM Bax, LH Hoefsloot… - Ophthalmology, 2015 - Elsevier
Objective To describe the phenotype and genotype of patients with early-onset Stargardt
disease. Design Retrospective cohort study. Participants Fifty-one Stargardt patients with …

Clinical and molecular analysis of Stargardt disease with preserved foveal structure and function

K Fujinami, PI Sergouniotis, AE Davidson… - American journal of …, 2013 - Elsevier
Purpose To describe a cohort of patients with Stargardt disease who show a foveal-sparing
phenotype. Design Retrospective case series. Methods The foveal-sparing phenotype was …

The role of multimodal imaging and vision function testing in ABCA4-related retinopathies and their relevance to future therapeutic interventions

S Al-Khuzaei, M Shah, CR Foster, J Yu… - Therapeutic …, 2021 - journals.sagepub.com
The aim of this review article is to describe the specific features of Stargardt disease and
ABCA4 retinopathies (ABCA4R) using multimodal imaging and functional testing and to …

Macular function and morphologic features in juvenile stargardt disease: longitudinal study

F Testa, P Melillo, V Di Iorio, A Orrico, M Attanasio… - Ophthalmology, 2014 - Elsevier
Purpose To evaluate disease progression in a cohort of patients with a clinical and genetic
diagnosis of Stargardt disease. Design Longitudinal cohort study. Participants A total of 56 …

Optical coherence tomography angiography findings in Stargardt disease

R Mastropasqua, L Toto, E Borrelli, L Di Antonio… - PLoS …, 2017 - journals.plos.org
Background to assess vessel density of superficial capillary plexus (SCP), deep capillary
plexus (DCP) and choriocapillaris (CC) in advanced Stargardt disease (STGD) using optical …

The value of two-field pattern electroretinogram in routine clinical electrophysiologic practice

E Lenassi, AG Robson, M Hawlina, GE Holder - Retina, 2012 - journals.lww.com
Purpose: To investigate the clinical use of the large-field pattern electroretinogram (PERG)
as an adjunct test to the International-standard PERG in an unselected sequential cohort of …

Natural History of Stargardt Disease: The Longest Follow-Up Cohort Study

J Sajovic, A Meglič, A Fakin, J Brecelj, M Šuštar Habjan… - Genes, 2023 - mdpi.com
Long-term natural history studies are important in rare disease research. This study aimed to
assess electrophysiological and fundus autofluorescence (FAF) progression rate in 18 …

Correlation between multifocal pattern electroretinography and Fourier-domain OCT in eyes with temporal hemianopia from chiasmal compression

MLR Monteiro, K Hokazono, LP Cunha… - Graefe's Archive for …, 2013 - Springer
Purpose To evaluate the correlation between multifocal pattern electroretinography
(mfPERG) and Fourier-domain optical coherence tomography (FD-OCT) with regard to …

Electroretinography as a Biomarker to Monitor the Progression of Stargardt Disease

J Sajovic, A Meglič, M Hawlina, A Fakin - International Journal of …, 2022 - mdpi.com
The aim of the present study is to determine how electroretinographic (ERG) responses
reflect age-related disease progression in the Stargardt disease (STGD1). The prospective …