Primary immunodeficiency diseases of adults: a review of pulmonary complication imaging findings
PA Grenier, AL Brun, E Longchampt, M Lipski… - European …, 2024 - Springer
Our objective in this review is to familiarize radiologists with the spectrum of initial and
progressive CT manifestations of pulmonary complications observed in adult patients with …
progressive CT manifestations of pulmonary complications observed in adult patients with …
[HTML][HTML] Clinical application of ultrashort echo-time MRI for lung pathologies in children
Lung magnetic resonance imaging (MRI) is considered to be challenging, because the low
proton density of the tissue, fast signal decay, and respiratory artefacts hamper adequate …
proton density of the tissue, fast signal decay, and respiratory artefacts hamper adequate …
Generating high-resolution synthetic CT from lung MRI with ultrashort echo times: initial evaluation in cystic fibrosis
A Longuefosse, J Raoult, I Benlala… - Radiology, 2023 - pubs.rsna.org
Background Lung MRI with ultrashort echo times (UTEs) enables high-resolution and
radiation-free morphologic imaging; however, its image quality is still lower than that of CT …
radiation-free morphologic imaging; however, its image quality is still lower than that of CT …
Effects of elexacaftor/tezacaftor/ivacaftor therapy in children with cystic fibrosis–a comprehensive assessment using lung clearance index, spirometry, and functional …
C Streibel, CC Willers, O Pusterla, G Bauman… - Journal of cystic …, 2023 - Elsevier
Background With improvement in supportive therapies and the introduction of cystic fibrosis
transmembrane conductance regulator (CFTR)-modulator treatment in patients with cystic …
transmembrane conductance regulator (CFTR)-modulator treatment in patients with cystic …
Longitudinal evaluation of bronchial changes in cystic fibrosis patients undergoing elexacaftor/tezacaftor/ivacaftor therapy using lung MRI with ultrashort echo‐times
M David, I Benlala, S Bui, T Benkert… - Journal of Magnetic …, 2024 - Wiley Online Library
Background Lung magnetic resonance imaging (MRI) with ultrashort echo‐times (UTE‐MRI)
allows high‐resolution and radiation‐free imaging of the lung structure in cystic fibrosis (CF) …
allows high‐resolution and radiation‐free imaging of the lung structure in cystic fibrosis (CF) …
Artificial intelligence-driven volumetric CT outcome score in cystic fibrosis: longitudinal and multicenter validation with/without modulators treatment
AI Hadj Bouzid, S Bui, I Benlala, P Berger, A Hutt… - European …, 2024 - Springer
Objectives Holistic segmentation of CT structural alterations with 3D deep learning has
recently been described in cystic fibrosis (CF), allowing the measurement of normalized …
recently been described in cystic fibrosis (CF), allowing the measurement of normalized …
Long-Term Impact of Lumacaftor/Ivacaftor Treatment on Cystic Fibrosis Disease Progression in Children 2–5 Years of Age Homozygous for F508del-CFTR: A Phase …
M Stahl, J Roehmel, M Eichinger… - Annals of the …, 2024 - atsjournals.org
Rationale: Clinical trials show that lumacaftor/ivacaftor (LUM/IVA) treatment has the potential
to modify early cystic fibrosis (CF) disease progression in children as young as 2 years of …
to modify early cystic fibrosis (CF) disease progression in children as young as 2 years of …
Artificial intelligence in computed tomography for quantifying lung changes in the era of CFTR modulators
Background Chest computed tomography (CT) remains the imaging standard for
demonstrating cystic fibrosis (CF) airway structural disease in vivo. However, visual scoring …
demonstrating cystic fibrosis (CF) airway structural disease in vivo. However, visual scoring …
Comparison of 3D UTE free‐breathing lung MRI with hyperpolarized 129Xe MRI in pediatric cystic fibrosis
S Munidasa, B Zanette, MP Dumas… - Magnetic …, 2025 - Wiley Online Library
Purpose To compare phase‐resolved functional lung (PREFUL) regional ventilation derived
from a free breathing 3D UTE radial MRI acquisition to hyperpolarized 129Xe‐MRI (Xe …
from a free breathing 3D UTE radial MRI acquisition to hyperpolarized 129Xe‐MRI (Xe …
Qualitative and quantitative evaluation of computed tomography changes in adults with cystic fibrosis treated with elexacaftor-tezacaftor-ivacaftor: a retrospective …
S Dettmer, O Weinheimer, A Sauer-Heilborn… - Frontiers in …, 2023 - frontiersin.org
Introduction: The availability of highly effective triple cystic fibrosis transmembrane
conductance regulator (CFTR) modulator combination therapy with elexacaftor–tezacaftor …
conductance regulator (CFTR) modulator combination therapy with elexacaftor–tezacaftor …