The biology of pulmonary exacerbations in bronchiectasis

F Amati, E Simonetta, A Gramegna… - European …, 2019 - Eur Respiratory Soc
Bronchiectasis is a heterogeneous chronic disease. Heterogeneity characterises
bronchiectasis not only in the stable state but also during exacerbations, despite evidence …

[HTML][HTML] The broad spectrum of lung diseases in primary antibody deficiencies

F Cinetto, R Scarpa, M Rattazzi… - European Respiratory …, 2018 - Eur Respiratory Soc
Human primary immunodeficiency diseases (PIDs) represent a heterogeneous group of
more than 350 disorders. They are rare diseases, but their global incidence is more relevant …

Non-infectious complications of common variable immunodeficiency: updated clinical spectrum, sequelae, and insights to pathogenesis

H Ho, C Cunningham-Rundles - Frontiers in immunology, 2020 - frontiersin.org
Non-infectious complications in common variable immunodeficiency (CVID) have emerged
as a major clinical challenge. Detailed clinical spectrum, organ-specific pathologies and …

Common variable immune deficiency and associated complications

S Gupta, D Pattanaik, G Krishnaswamy - Chest, 2019 - Elsevier
Common variable immunodeficiency disorders refer to a relatively common primary immune
deficiency group of diseases that present with infectious and inflammatory complications …

[HTML][HTML] BAFF-driven B cell hyperplasia underlies lung disease in common variable immunodeficiency

PJ Maglione, G Gyimesi, M Cols, L Radigan, HM Ko… - JCI insight, 2019 - ncbi.nlm.nih.gov
BACKGROUND. Common variable immunodeficiency (CVID) is the most common
symptomatic primary immunodeficiency and is frequently complicated by interstitial lung …

State-of-the-art diagnostic evaluation of common variable immunodeficiency

TK Lee, JD Gereige, PJ Maglione - Annals of Allergy, Asthma & Immunology, 2021 - Elsevier
Objective To summarize the current understanding of diagnostic and postdiagnostic
evaluation of common variable immunodeficiency (CVID). Data Sources PubMed Central …

Diagnostic testing for interstitial lung disease in common variable immunodeficiency: a systematic review

HM Bintalib, A van de Ven, J Jacob… - Frontiers in …, 2023 - frontiersin.org
Introduction Common variable immunodeficiency related interstitial lung disease (CVID-ILD,
also referred to as GLILD) is generally considered a manifestation of systemic immune …

B cell dysregulation in common variable immunodeficiency interstitial lung disease

EM Matson, ML Abyazi, KA Bell, KM Hayes… - Frontiers in …, 2021 - frontiersin.org
Common variable immunodeficiency (CVID) is the most frequently diagnosed primary
antibody deficiency. About half of CVID patients develop chronic non-infectious …

Multimorbidity in bronchiectasis: a systematic scoping review

I Marsland, R Sobala, A De Soyza… - ERJ Open …, 2023 - Eur Respiratory Soc
Introduction Multimorbidity, the coexistence of two or more chronic conditions, has been
extensively studied in certain disease states. Bronchiectasis aetiology is complex and …

Histology of interstitial lung disease in common variable immune deficiency

F Dhalla, DJM Lochlainn, H Chapel… - Frontiers in …, 2020 - frontiersin.org
Interstitial lung disease (ILD) is an important non-infectious complication in several primary
immune deficiencies. In common variable immune deficiency (CVID) it is associated with …