Abstract IgG4-related disease (IgG4-RD) is a recently recognized fibro-inflammatory
disorder that can affect almost any organ. Common presentations include major salivary and …

Eosinophilic granulomatosis with polyangiitis is characterized by asthma, blood and tissue
eosinophilia and small-vessel vasculitis. The clinical presentation is variable, but two main …

Antibodies of IgG4 subclass are exceptional players of the immune system, as they are
considered to be immunologically inert and functionally monovalent, and as such may be …

Abstract Objective Immunoglobulin G4 (IgG4)-related disease is a systemic chronic
fibroinflammatory disease that can affect almost every organ of the body. IgG4-related …

The most representative kidney lesion of IgG4-related disease (IgG4-RD) is plasma cell-rich
tubulointerstitial nephritis (TIN) with distinctive imaging findings including multiple low …

Anti-neutrophil cytoplasmic antibodies (ANCA) are a group of autoantibodies, predominantly
IgG, involved in the pathogenesis of several autoimmune disorders, detected either through …

Objective To analyse the ocular manifestations of patients with GPA, their treatment and
outcome. Methods Retrospective cohort study performed at the National Referral Center for …

Background IgG4-related kidney disease is a major manifestation of IgG4-related disease, a
systemic fibroinflammatory disorder. However, the clinical and prognostic kidney-related …

Anti-neutrophil cytoplasmic antibody (ANCA)-associated vasculitis (AAV) is a form of
necrotizing vasculitis with few or no immune deposits. It primarily affects small and medium …

Autoimmune pancreatitis (AIP), a unique subtype of pancreatitis, is often accompanied by
systemic inflammatory disorders. AIP is classified into two distinct subtypes on the basis of …