Simultaneous liver kidney transplantation

AK Singal, S Ong, SK Satapathy… - Transplant …, 2019 - Wiley Online Library
Kidney injury is frequently seen in patients with end‐stage liver disease from cirrhosis and
liver failure. Among selected patients, simultaneous liver kidney (SLK) transplantation …

Early clinical management of autosomal recessive polycystic kidney disease

MC Liebau - Pediatric Nephrology, 2021 - Springer
Autosomal recessive polycystic kidney disease (ARPKD) is a rare but highly relevant
disorder in pediatric nephrology. This genetic disease is mainly caused by variants in the …

Clinical courses and complications of young adults with autosomal recessive polycystic kidney disease (ARPKD)

K Burgmaier, S Kilian, B Bammens, T Benzing… - Scientific Reports, 2019 - nature.com
Autosomal recessive polycystic kidney disease (ARPKD) is a severe pediatric hepatorenal
disorder with pronounced phenotypic variability. A substantial number of patients with early …

[HTML][HTML] Polycystic kidney disease, autosomal recessive

WE Sweeney, ED Avner - GeneReviews®[Internet], 2019 - ncbi.nlm.nih.gov
Autosomal recessive polycystic kidney disease–PKHD1 (ARPKD-PKHD1) is characterized
by primary involvement of the kidneys and liver with mostly secondary effects seen in other …

Combined and sequential liver–kidney transplantation in children

R Grenda, P Kaliciński - Pediatric Nephrology, 2018 - Springer
Combined and sequential liver–kidney transplantation (CLKT and SLKT) is a definitive
treatment in children with end-stage organ failure. There are two major indications:-terminal …

Diseases of the primary cilia: A clinical characteristics review

B Alzarka, O Charnaya, M Gunay-Aygun - Pediatric Nephrology, 2024 - Springer
Ciliopathies encompass a broad spectrum of diseases stemming from dysfunction of the
primary (non-motile) cilia, present on almost all cells in the human body. These disorders …

Autosomal Recessive Polycystic Kidney Disease: Diagnosis, Prognosis, and Management

K Burgmaier, IJ Broekaert, MC Liebau - Advances in Kidney Disease and …, 2023 - Elsevier
Autosomal recessive polycystic kidney disease (ARPKD) is the rare and usually early-onset
form of polycystic kidney disease with a typical clinical presentation of enlarged cystic …

Long-term kidney and liver outcome in 50 children with autosomal recessive polycystic kidney disease

G Dorval, O Boyer, A Couderc, JD Delbet, L Heidet… - Pediatric …, 2021 - Springer
Background Autosomal recessive polycystic kidney disease (ARPKD) is a rare ciliopathy
characterized by congenital hepatic fibrosis and cystic kidney disease. Lack of data about …

Design of two ongoing clinical trials of tolvaptan in the treatment of pediatric patients with autosomal recessive polycystic kidney disease

D Mekahli, MC Liebau, MA Cadnapaphornchai… - BMC nephrology, 2023 - Springer
Purpose Autosomal recessive polycystic kidney disease (ARPKD) is a hereditary condition
characterized by massive kidney enlargement and developmental liver defects. Potential …

Long-term outcome of transjugular intrahepatic portosystemic shunt for portal hypertension in autosomal recessive polycystic kidney disease

S Verbeeck, D Mekahli, D Cassiman, G Maleux… - Digestive and Liver …, 2018 - Elsevier
Background Autosomal recessive polycystic kidney disease (ARPKD) with congenital
hepatic fibrosis (CHF) causes portal hypertension and its complications. A transjugular …