In the absence of contemporary, population-based epidemiological studies, estimates of the
incidence and prevalence of the inherited cardiomyopathies have been derived from …

In this paper the Working Group on Myocardial and Pericardial Disease proposes a revised
definition of dilated cardiomyopathy (DCM) in an attempt to bridge the gap between our …

Arrhythmogenic cardiomyopathy (ACM) is an arrhythmogenic disorder of the myocardium
not secondary to ischemic, hypertensive, or valvular heart disease. ACM incorporates a …

Background: Mutations in desmoplakin (DSP), the primary force transducer between cardiac
desmosomes and intermediate filaments, cause an arrhythmogenic form of cardiomyopathy …

Background: Cardiomyopathies are a heterogeneous group of pathologies characterized by
structural and functional alterations of the heart. Aims: The purpose of this narrative review is …

Arrhythmogenic cardiomyopathy is an inherited heart muscle disorder, predisposing to
sudden cardiac death, particularly in young patients and athletes. Pathological features …

Background—In 1994, an International Task Force proposed criteria for the clinical
diagnosis of arrhythmogenic right ventricular cardiomyopathy/dysplasia (ARVC/D) that …

Aims We sought to determine the influence of genotype on clinical course and arrhythmic
outcome among arrhythmogenic right ventricular dysplasia/cardiomyopathy (ARVD/C) …

Arrhythmogenic right ventricular cardiomyopathy is a rare inherited heart-muscle disease
that is a cause of sudden death in young people and athletes. Causative mutations in genes …

Dilated cardiomyopathy (DCM) is an umbrella term entailing a wide variety of genetic and
non-genetic etiologies, leading to left ventricular systolic dysfunction and dilatation, not …