Lymphangioleiomyomatosis: pathogenesis, clinical features, diagnosis, and management
Lymphangioleiomyomatosis (LAM) is a slowly progressive, low-grade, metastasising
neoplasm of women, characterised by infiltration of the lung parenchyma with abnormal …
neoplasm of women, characterised by infiltration of the lung parenchyma with abnormal …
Lymphangioleiomyomatosis
SR Johnson - Orphan lung diseases: a clinical guide to rare lung …, 2023 - Springer
Lymphangioleiomyomatosis (LAM) is a rare multisystem disease which predominantly
affects women. The disease occurs both sporadically and is common in women with …
affects women. The disease occurs both sporadically and is common in women with …
Official American Thoracic Society/Japanese Respiratory Society clinical practice guidelines: lymphangioleiomyomatosis diagnosis and management
FX McCormack, N Gupta, GR Finlay… - American journal of …, 2016 - atsjournals.org
Background: Lymphangioleiomyomatosis (LAM) is a rare cystic lung disease that primarily
affects women. The purpose of these guidelines is to provide recommendations for the …
affects women. The purpose of these guidelines is to provide recommendations for the …
The NHLBI LAM registry: prognostic physiologic and radiologic biomarkers emerge from a 15-year prospective longitudinal analysis
N Gupta, HS Lee, JH Ryu, AM Taveira-DaSilva… - Chest, 2019 - Elsevier
Background The natural history of lymphangioleiomyomatosis (LAM) is mainly derived from
retrospective cohort analyses, and it remains incompletely understood. A National Institutes …
retrospective cohort analyses, and it remains incompletely understood. A National Institutes …
Pulmonary manifestations in tuberous sclerosis complex
Tuberous sclerosis complex has manifestations in many organ systems, including brain,
heart, kidney, skin, and lung. The primary manifestations in the lung are …
heart, kidney, skin, and lung. The primary manifestations in the lung are …
Sustained effects of sirolimus on lung function and cystic lung lesions in lymphangioleiomyomatosis
J Yao, AM Taveira-DaSilva, AM Jones… - American journal of …, 2014 - atsjournals.org
Rationale: Sirolimus therapy stabilizes lung function and reduces the size of chylous
effusions and lymphangioleiomyomas in patients with lymphangioleiomyomatosis …
effusions and lymphangioleiomyomas in patients with lymphangioleiomyomatosis …
[HTML][HTML] Tuberous sclerosis complex for the pulmonologist
Y Rebaine, M Nasser, B Girerd… - European Respiratory …, 2021 - Eur Respiratory Soc
Tuberous sclerosis complex (TSC) is a rare multisystem genetic disorder affecting almost all
organs with no sex predominance. TSC has an autosomal-dominant inheritance and is …
organs with no sex predominance. TSC has an autosomal-dominant inheritance and is …
Lymphangioleiomyomatosis
KF Xu, W Xu, S Liu, J Yu, X Tian, Y Yang… - … in Respiratory and …, 2020 - thieme-connect.com
Lymphangioleiomyomatosis (LAM) is a slow albeit progressive rare neoplastic disease
featured with diffuse thin-walled cysts in lungs and angiomyolipomas in kidneys. LAM affects …
featured with diffuse thin-walled cysts in lungs and angiomyolipomas in kidneys. LAM affects …
Minireview: lymphangioleiomyomatosis (LAM): the “other” steroid-sensitive cancer
Lymphangioleiomyomatosis (LAM) is a devastating rare lung disease affecting primarily
childbearing age women in which tumors consisting of abnormal smooth-muscle-like cells …
childbearing age women in which tumors consisting of abnormal smooth-muscle-like cells …
New insights in lymphangioleiomyomatosis and pulmonary Langerhans cell histiocytosis
O Torre, D Elia, A Caminati… - European Respiratory …, 2017 - Eur Respiratory Soc
Lymphangioleiomyomatosis (LAM) and pulmonary Langerhans cell histiocytosis (PLCH) are
rare diseases that lead to progressive cystic destruction of the lungs. Despite their distinctive …
rare diseases that lead to progressive cystic destruction of the lungs. Despite their distinctive …