Chronic thromboembolic pulmonary hypertension (CTEPH): updated recommendations from the Cologne Consensus Conference 2018

H Wilkens, S Konstantinides, IM Lang, AC Bunck… - International journal of …, 2018 - Elsevier
Chronic thromboembolic pulmonary hypertension (CTEPH) is a subgroup of pulmonary
hypertension that differs from all other forms of PH in terms of its pathophysiology, patient …

A comprehensive review on the diagnosis and management of intimal sarcoma of the pulmonary artery

T Assi, J Kattan, E Rassy, T Moussa… - Critical reviews in …, 2020 - Elsevier
Only a few hundred cases of intimal sarcomas of pulmonary artery (ISPA) were reported on
the literature. Diagnosis of this rare entity is a challenging dilemma with the need for a high …

Evaluation and management of patients with chronic thromboembolic pulmonary hypertension-consensus statement from the ISHLT

M de Perrot, D Gopalan, D Jenkins, IM Lang… - The Journal of Heart and …, 2021 - Elsevier
ISHLT members have recognized the importance of a consensus statement on the
evaluation and management of patients with chronic thromboembolic pulmonary …

Intimal sarcoma of the great vessels

AM Ropp, AP Burke, SJ Kligerman, JS Leb… - Radiographics, 2021 - pubs.rsna.org
Intimal sarcomas of the pulmonary artery and aorta are rare entities with a poor prognosis. In
many instances, pulmonary artery sarcomas are misinterpreted as acute or chronic …

[HTML][HTML] Clinical features and surgical outcomes of pulmonary artery sarcoma

K Yin, Z Zhang, R Luo, Y Ji, D Zheng, Y Lin… - The Journal of thoracic …, 2018 - Elsevier
Objective Pulmonary artery sarcoma is an exceedingly rare malignancy. There is a lack of
consensus regarding its diagnosis and treatment. We reviewed our experience in the …

Mimickers of chronic thromboembolic pulmonary hypertension on imaging tests: a review

S Narechania, R Renapurkar… - Pulmonary …, 2020 - journals.sagepub.com
Chronic thromboembolic pulmonary hypertension (CTEPH) is caused by mechanical
obstruction of large pulmonary arteries secondary to one or more episodes of pulmonary …

Systemic treatments in MDM2 positive intimal sarcoma: a multicentre experience with anthracycline, gemcitabine, and pazopanib within the World Sarcoma Network

AM Frezza, T Assi, S Lo Vullo, E Ben‐Ami, A Dufresne… - Cancer, 2020 - Wiley Online Library
Background Intimal sarcoma (InS) is an exceedingly rare neoplasm with an unfavorable
prognosis, for which new potentially active treatments are under development. We report on …

Clinical presentation and surgical treatment of primary pulmonary artery sarcoma

L Deng, J Zhu, J Xu, S Guo, S Liu… - … and thoracic surgery, 2018 - academic.oup.com
OBJECTIVES Pulmonary artery sarcoma (PAS) is a rare and devastating disease. The
diagnosis modality and optimal surgical strategy remain unclear. The aim of this study was …

Multimodal approach of pulmonary artery intimal sarcoma: a single‐institution experience

S Secondino, V Grazioli, F Valentino, M Pin… - Sarcoma, 2017 - Wiley Online Library
Introduction. Pulmonary artery sarcoma (PAS) is a rare tumor, whose therapeutic approach
is mainly based on surgery, either pneumonectomy or pulmonary endarterectomy (PEA) …

Differential diagnosis of pulmonary artery sarcoma and central chronic pulmonary thromboembolism using CT and MR images

MX Liu, ZH Ma, T Jiang, XJ Guo, FF Yu… - Heart, Lung and …, 2018 - Elsevier
Background Clinical and imaging manifestations are similar in pulmonary artery sarcomas
(PAS) and thromboembolic diseases, especially central chronic pulmonary …