Defining global strategies to improve outcomes in sickle cell disease: a Lancet Haematology Commission

FB Piel, DC Rees, MR DeBaun, O Nnodu… - The Lancet …, 2023 - thelancet.com
Executive summary All over the world, people with sickle cell disease (an inherited
condition) have premature deaths and preventable severe chronic complications, which …

Delayed hemolytic transfusion reaction in adult sickle‐cell disease: presentations, outcomes, and treatments of 99 referral center episodes

A Habibi, A Mekontso‐Dessap… - American Journal of …, 2016 - Wiley Online Library
Delayed hemolytic transfusion reaction (DHTR) is one of the most feared complications of
sickle‐cell disease (SCD). We retrospectively analyzed the clinical and biological features …

Depression in adults with sickle cell disease: a systematic review of the methodological issues in assessing prevalence of depression

D Oudin Doglioni, V Chabasseur, F Barbot… - BMC psychology, 2021 - Springer
Background Sickle cell disease (SCD) as other chronic medical conditions is commonly
complicated by depression or other psychiatric symptoms. Results reported in studies …

Managing pregnancy in patients with sickle cell disease from a transfusion perspective

A Habibi, A Benachi, E Lecarpentier - Hematology, 2023 - ashpublications.org
Advances in the management of sickle cell disease (SCD) have made it possible for most
female patients (whether homozygous or compound heterozygous) to reach childbearing …

Managing sickle cell disease and related complications in pregnancy: results of an international Delphi panel

D Sharma, I Kozanoğlu, KI Ataga, A Benachi… - Blood …, 2024 - ashpublications.org
Data to guide evidence-based management of pregnant people with sickle cell disease
(SCD) are limited. This international Delphi panel aimed to identify consensus among …

Nationwide retrospective study of critically ill adults with sickle cell disease in France

M Agbakou, A Mekontso-Dessap, M Pere, G Voiriot… - Scientific Reports, 2021 - nature.com
Little is known about patients with sickle cell disease (SCD) who require intensive care unit
(ICU) admission. The goals of this study were to assess outcomes in patients admitted to the …

Syndrome thoracique aigu chez les patients drépanocytaires adultes

G Cheminet, A Mekontso-Dessap, J Pouchot… - La Revue de Médecine …, 2022 - Elsevier
Résumé La drépanocytose, maladie génétique due à une mutation du gène de la β-globine,
est une pathologie systémique fréquente en France, caractérisée par de multiples …

Unveiling mortality risk factors in paediatric sickle cell disease patients during acute crises in the Democratic Republic of the Congo

PM Boma, SL Ngimbi, JM Kindundu, JI Wela… - Blood cells, molecules …, 2024 - Elsevier
Sickle cell disease (SCD) is a significant health burden in the Democratic Republic of the
Congo (DRC). This study aims to identify predictive factors of mortality in SCD children …

Psychometric characteristics of the Revised Illness Perception Questionnaire (IPQ-R) in adults with sickle cell disease

D Oudin Doglioni… - Health Psychology …, 2022 - Taylor & Francis
Objective Sickle cell disease (SCD) is the most frequent monogenic disease worldwide.
Psychological and behavioural factors are often reported as playing a significant role in …

Pregnancy outcomes among patients with sickle cell disease in Brazzaville

FO Galiba Atipo Tsiba, C Itoua, C Ehourossika… - Anemia, 2020 - Wiley Online Library
Introduction. Sickle cell disease (SCD) is one of the most common genetic diseases in the
world. It combines, in its homozygous form, chronic hemolytic anemia, vasoocclusive …