Abstract Purpose of Review The field of neuroendocrine oncology has changed much since
the time of Oberndorfer first described and coined the term carcinoid. The purpose of this …

Von Hippel-Lindau disease is an autosomal dominant disorder characterised by renal cell
carcinomas, pancreatic neuroendocrine tumours, central nervous system …

In this article, we present a Von Hippel–Lindau (VHL) patient with synchoronus bilateral
testicular metastasis from renal cell carcinoma (RCC). A 50 year-old man, a known case of …

Von Hippel–Lindau (vHL) is a hereditary disease characterized by the development of
benign and malignant tumors across multiple organ systems. It is seen in approximately 1 in …

Cysts are epithelial-lined, hollow cavities that are usually filled with fluid but can also contain
blood, pus, air, or other solid material. Cystic kidney disease is an umbrella term that …

Bone is reported to be one of the most common sites of metastasis. Acrometastasis is an
extremely rare situation and accounts for approximately 0.1% of all metastatic lesions to the …

A relevant number of neuroendocrine neoplasms (NENs) show a hereditary background
being associated with a genetic endocrine neoplastic syndrome. Multiple endocrine …

A subgroup of neuroendocrine neoplasms (NENs) show a hereditary background and occur
in the context of genetic endocrine neoplastic syndromes, such as multiple endocrine …

Background Steroid cell tumours of the ovary account for approximately 0.1% of all ovarian
tumours. Association of these tumours with Von Hippel–Lindau syndrome is an extremely …

Abstract Von Hippel–Lindau syndrome (VHL-syndrome) is a rare hereditary tumor syndrome
predisposing affected patients to hemangioblastomas in the central nervous system (CNS) …