Investigation and management of Wilson's disease: a practical guide from the British Association for the Study of the Liver

S Shribman, T Marjot, A Sharif… - The Lancet …, 2022 - thelancet.com
Wilson's disease is an autosomal-recessive disorder of copper metabolism with hepatic,
neurological, psychiatric, ophthalmological, haematological, renal, and rheumatological …

North American Society for Pediatric Gastroenterology, Hepatology, and Nutrition position paper on the diagnosis and management of pediatric acute liver failure

JE Squires, EM Alonso, SH Ibrahim… - Journal of pediatric …, 2022 - journals.lww.com
Pediatric acute liver failure (PALF) is a rare, rapidly progressive clinical syndrome with
significant morbidity and mortality. The phenotype of PALF manifests as abrupt onset liver …

Acute liver failure in children

DG Sabapathy, MS Desai - Pediatric Clinics, 2022 - pediatric.theclinics.com
The liver is the largest solid organ in a human body comprising w2% of the bodyweight, and
uniquely receiving blood supply from two sources: the portal vein (w75%) and hepatic artery …

Diagnostic approach to acute liver failure in children: a position paper by the SIGENP liver disease working group

A Di Giorgio, E Bartolini, PL Calvo, M Cananzi… - Digestive and Liver …, 2021 - Elsevier
Acute liver failure (ALF) is a clinical condition characterized by the abrupt onset of
coagulopathy and biochemical evidence of hepatocellular injury, leading to rapid …

Outcome of 200 pediatric living donor liver transplantations in India

N Mohan, S Karkra, A Rastogi, MS Dhaliwal… - Indian pediatrics, 2017 - Springer
Objective To describe our experience of pediatric living donor liver transplantation from India
over a period of 12 years. Materials and Methods A retrospective analysis of 200 living …

Lactate and lactate: pyruvate ratio in the diagnosis and outcomes of pediatric acute liver failure

AG Feldman, RJ Sokol, RM Hardison, EM Alonso… - The Journal of …, 2017 - Elsevier
Objectives To assess the accuracy of blood lactate and lactate: pyruvate molar ratio (L: P) as
a screen for mitochondrial, respiratory chain, or fatty acid oxidation disorders in children with …

Indian national association for the study of the liver consensus statement on acute liver failure (Part 1): epidemiology, pathogenesis, presentation and prognosis

AC Anand, B Nandi, SK Acharya, A Arora… - Journal of Clinical and …, 2020 - Elsevier
Acute liver failure (ALF) is an infrequent, unpredictable, potentially fatal complication of
acute liver injury (ALI) consequent to varied etiologies. Etiologies of ALF as reported in the …

Indian national association for the study of liver consensus statement on acute liver failure (Part-2): management of acute liver failure

AC Anand, B Nandi, SK Acharya, A Arora… - Journal of Clinical and …, 2020 - Elsevier
Acute liver failure (ALF) is not an uncommon complication of a common disease such as
acute hepatitis. Viral hepatitis followed by antituberculosis drug–induced hepatotoxicity are …

Demographics, aetiology and outcome of paediatric acute liver failure in Singapore

FK Chiou, V Logarajah, CWW Ho… - Singapore Medical …, 2022 - journals.lww.com
Methods: A retrospective review was performed of patients aged 0–18 years who were
diagnosed with PALF from 2007 to 2019. PALF was defined by: absence of chronic liver …

Liver involvement in congenital disorders of glycosylation: a systematic review

R Colantuono, E D'Acunto, D Melis… - Journal of pediatric …, 2021 - journals.lww.com
An ever-increasing number of disturbances in glycosylation have been described to underlie
certain unexplained liver diseases presenting either almost isolated or in a multi-organ …