Systemic amyloidoses are rare, complex diseases caused by misfolding of autologous
protein. The presence of heart involvement is the most important prognostic determinant …

Aims In transthyretin amyloid (ATTR) amyloidosis various principal phenotypes have been
described: cardiac, neuropathic, or a mixed cardiac and neuropathic. In addition, two …

RESULTS Clinical Presentation The proband (Figure 1, II-4), a 45-year-old woman, was
seen in the Amyloidosis Center at Boston University School of Medicine for evaluation. At …

Light chain amyloidosis needs to be considered in the differential diagnosis of patients with
nondiabetic nephrotic range proteinuria, unexplained fatigue or heart failure with preserved …

Amyloidosis is a group of disorders characterised by the accumulation of extracellular
deposits of insoluble protein aggregates. Clinical management depends on the accurate …

Heart failure is a progressive disease, representing a growing cause of morbidity,
hospitalization, and mortality. An increasingly common type of heart failure with preserved …

Purpose Cardiac amyloidosis is a rare and still underdiagnosed disease leading a poor
prognosis. We reviewed the literature regarding non-invasive imaging of cardiac …

Two main types of cardiac amyloidosis (CA) exist, as a result of either aberrant plasma cell
production of misfolded monoclonal light chains, known as immunoglobulin light chain …

RESULTS Clinical Presentation The proband (Figure 1, II-4), a 45-year-old woman, was
seen in the Amyloidosis Center at Boston University School of Medicine for evaluation. At …

Cardiomyopathies are little known to internists and general practitioners (GPs), and not
always able to arouse the interest of cardiologists. Probably, this happens because …