Purpose Patients with primary immunodeficiency diseases (PIDD) may present with
recurrent infections affecting different organs, organ-specific inflammation/autoimmunity, and …

Cutaneous manifestations are common in primary immune deficiency diseases, affecting
between 40% and 70% of patients with diagnosed primary immune deficiency. Skin …

Skin manifestations are prevalent in primary immunodeficiency disorders (PID). In a large
proportion of patients, they manifest as presenting signs and serve as important factors for …

This is Part 2 of an updated follow-up review of the World Allergy Organization (WAO)
position paper on the diagnosis and treatment of urticaria and angioedema. Since that …

Primary immunodeficiency diseases (PID s) are characterized by an increased risk of
infections, autoimmunity, autoinflammation, malignancy, and allergic disorders. Skin …

Primary immune deficiency diseases characteristically present with recurrent, severe, or
unusual infections. These infections may often involve the skin, with mucocutaneous …

Inborn errors of immunity associated with atopy (IEIs-A) are a group of inherited monogenic
disorders that occur with immune dysregulation and frequent skin involvement. Several …

Abstract Background: The IL-12/IFN-γ axis plays a vital role in the control of
intramacrophagic pathogens including Leishmania infections. Objective: The aim of this …

Background and Objectives Reports on skin manifestations in inborn errors of immunity (IEI)
are based on retrospective analysis, small series, or isolated case reports. The present …

Skin manifestations are frequent among patients with primary immunodeficiency diseases
(PIDs). Their prevalence varies according to the type of immunodeficiency. This review …