Cystic fibrosis (CF) is the most common autosomal recessive disease in the Caucasian
population. Cystic fibrosis-related liver disease (CFLD) is defined as the pathogenesis …

Cystic fibrosis liver disease (CFLD) is characterised by a wide heterogenity of manifestations
and severity. It represents a major cause of morbidity in people with cystic fibrosis (PwCF) …

Cystic fibrosis (CF) may cause a spectrum of hepatobiliary complications, including portal
hypertension, multilobular cirrhosis, and liver failure. Current guidelines on the detection …

The broad spectrum of hepatobiliary involvement in cystic fibrosis (CF) has been commonly
referred to as cystic fibrosis liver disease (CFLD). However, differences in the definitions of …

Abstract Background and Objective Reliable markers are needed for early diagnosis and
follow-up of liver disease in Cystic Fibrosis (CF). The objective was to evaluate the …

Background Complications from liver cirrhosis are a leading cause of death in children with
cystic fibrosis. Identifying children at risk for developing liver cirrhosis and halting its …

Background There are limited studies to date on the effects of elexacaftor/tezacaftor/ivacaftor
(E/T/I) on markers of liver fibrosis in adults with cystic fibrosis (CF). This study aims to …

Background Nodular liver (NOD) in cystic fibrosis (CF) suggests advanced CF liver disease
(aCFLD); little is known about progression of liver disease (LD) after detection of …

Background & Aims A practical, inexpensive, and non-invasive biomarker of liver fibrosis is
needed as a reliable screening test for cystic fibrosis-associated liver disease (CFLD) …

Cystic fibrosis liver disease in the post-modulator era : Current Opinion in Pulmonary Medicine
Cystic fibrosis liver disease in the post-modulator era : Current Opinion in Pulmonary Medicine …