Background Malnutrition is both a frequent feature and a comorbidity of cystic fibrosis (CF),
with nutritional status strongly associated with pulmonary function and survival. Nutritional …

Introduction: Cystic fibrosis (CF) is a severe, progressive, multisystemic disease that is
caused by mutations in the cystic fibrosis transmembrane conductance regulator gene …

Pancreatic exocrine insufficiency (PEI) is often observed in patients with pancreatic
diseases, including chronic pancreatitis, cystic fibrosis, and tumors, or after surgical …

Objectives In high-income countries hepatitis E virus (HEV) is an uncommonly diagnosed
porcine-derived zoonoses. After identifying disproportionate chronic HEV infections in …

Poor clinical outcomes in cystic fibrosis are often associated with undernutrition. Normal
growth and development should be achieved in cystic fibrosis, and nutritional counseling is …

The Best Pharmaceuticals for Children Act (BPCA) and the Pediatric Research Equity Act
(PREA) were designed to encourage more pediatric studies of drugs used for children. The …

Management of chronic pancreatitis is challenging and requires a personalized approach
(Fig. 12). Early diagnosis of CP plays a significant role in the natural history of the disease …

Pancreatic exocrine insufficiency (PEI) is defined as a reduction in pancreatic exocrine
secretion below the level that allows the normal digestion of nutrients. Pancreatic disease …

Background: Alkalinized Viokase pancreatic enzyme tablets restored patency to 71.9% of
occluded Dobhoff tubes in a prospective study. After removal of Viokase tablets from the US …

Cystic fibrosis (CF) is an inherited chronic disease that affects approximately 30,000 children
and adults in the United States and approximately 80,000 individuals worldwide. 1 CF is …