Over the past decade, as the majority of patients with single ventricle anatomy who have
undergone the Fontan operation reach adulthood, a newly recognized disease process …

Because of remarkable surgical and medical advances over the past several decades, there
are growing numbers of infants and children living with single ventricle congenital heart …

Background: Long-term outcomes of Fontan patients who survive to age≥ 16 years have
not been well characterized. The Australian and New Zealand Fontan Registry (ANZFR) …

In patients with a functionally univentricular heart, the Fontan strategy achieves separation of
the systemic and pulmonary circulation and reduction of ventricular volume overload …

Objective Infants with congenital heart disease (CHD) often experience growth failure prior
to surgery, which is associated with increased paediatric-intensive-care unit length of stay …

Stents are tubular meshed endoprostheses implanted mini-invasively through a
transcatheter intervention to guarantee the patency of body conduits, mainly in …

Background Single ventricle (SV) congenital heart disease is fatal without intervention, and
eventual heart failure is a major cause of morbidity and mortality. Although there are no …

The single ventricle patient population comprises the most complex cohort presenting to the
cardiac transplant team, in terms of demographics, anatomic substrate, and unique …

OBJECTIVES Adults with failing Fontan circulation (FFC) represent a heterogeneous, high-
risk group for cardiac transplantation with poor reported outcomes. We studied the impact of …

D. Woodrow Benson, MD, PhD1, Lisa J. Martin, PhD2, and Cecilia W. Lo, PhD3 Hypoplastic
left heart syndrome (HLHS; MIM# 241550) is a severe congenital heart defect (CHD) …