Cognitive reserve protects ALS‐typical cognitive domains: A longitudinal study.

AGM Temp, E Kasper, J Machts… - Annals of Clinical …, 2022 - Wiley Online Library
Abstract Background and Objectives To determine whether cognitive reserve (CR) as
measured by verbal intelligence quotient, educational length, and achievement protects …

[HTML][HTML] Cognitive reserve and regional brain volume in amyotrophic lateral sclerosis

AGM Temp, J Prudlo, S Vielhaber, J Machts… - Cortex, 2021 - Elsevier
Objective We investigated whether cognitive reserve measured by education and premorbid
IQ allows amyotrophic lateral sclerosis patients to compensate for regional brain volume …

Cognitive impairment in adult patients with 5q-associated spinal muscular atrophy

K Kizina, Y Akkaya, D Jokisch, B Stolte, A Totzeck… - Brain Sciences, 2021 - mdpi.com
In previous studies, a below-average, average, or above-average intelligence quotient (IQ)
in children with SMA was detected but, aside from a severe physical disability, the cognitive …

Exploring variability in cognitive functioning in patients with spinal muscular atrophy: a scoping review

G Giannotta, M Ruggiero, M De Rinaldis… - Neurological …, 2024 - Springer
The cognitive functioning of individuals with spinal muscular atrophy (SMA) is not well
understood, prompting a call for more research to better grasp cognitive involvement in …

Cognitive impairment in Chinese adult patients with type III spinal muscular atrophy without disease-modifying treatment

Y Hu, L Wei, A Li, T Liu, Y Jiang, C Xie… - Frontiers in …, 2023 - frontiersin.org
Objective Spinal muscular atrophy (SMA) is a neurodegenerative disorder characterized by
the degeneration of motor neurons in the spinal cord. It remains uncertain whether the …

Behavioral problems in infants and young children with spinal muscular atrophy and their siblings: A cross-sectional study

PK Panda, A Ramachandran, PK Verma… - European Journal of …, 2023 - Elsevier
Introduction Older children and adults with spinal muscular atrophy (SMA) have been shown
to have more anxiety, depression, and other behavioral problems in a few studies. But no …

Cognitive performance of adult patients with SMA before and after treatment initiation with nusinersen

M Vidovic, M Freigang, E Aust, K Linse, D Petzold… - BMC neurology, 2023 - Springer
Background Spinal muscular atrophy (SMA) is a genetic neuromuscular disease caused by
mutations of the SMN1 gene. Deficient SMN protein causes irreversible degeneration of …

Validity and reliability of the German multidimensional fatigue inventory in spinal muscular atrophy

C Binz, A Osmanovic, NH Thomas… - Annals of Clinical …, 2022 - Wiley Online Library
Objective Fatigue is a common and burdensome symptom of spinal muscular atrophy. Given
its complex interactions, different dimensions of fatigue need to be investigated. The …

Loss of “insight” into behavioral changes in ALS: Differences across cognitive profiles

AGM Temp, E Kasper, S Vielhaber, J Machts… - Brain and …, 2022 - Wiley Online Library
Objective Behavioral impairment occurs in amyotrophic lateral sclerosis (ALS) and ALS–
fronto‐temporal dementia (ALS‐FTD). It has been proposed that ALS patients without FTD …

[HTML][HTML] Cognition and communication in patients with spinal muscular atrophy: A systematic review

S Akodad, D De Smedt, S Baijot, H Stevens… - Heliyon, 2024 - cell.com
Cognition and communication in patients with spinal muscular atrophy: A systematic review:
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