How I diagnose and manage VEXAS syndrome
A Hagiya, IN Siddiqi, E Wang… - American Journal of …, 2024 - academic.oup.com
Objectives To discuss VEXAS (vacuoles, E1 enzyme, X-linked, autoinflammatory, somatic)
syndrome, including the clinical and pathologic features, diagnostic challenges, and …
syndrome, including the clinical and pathologic features, diagnostic challenges, and …
Venous and arterial thrombosis in patients with VEXAS syndrome
Y Kusne, A Ghorbanzadeh, A Dulau-Florea… - Blood, 2024 - ashpublications.org
Abstract VEXAS (vacuoles, E1 enzyme, X-linked, autoinflammatory, somatic) syndrome,
caused by somatic mutations in UBA1, is an autoinflammatory disorder with diverse systemic …
caused by somatic mutations in UBA1, is an autoinflammatory disorder with diverse systemic …
VEXAS syndrome: an adult-onset autoinflammatory disorder with underlying somatic mutation
I Kötter, M Krusche - Current Opinion in Rheumatology, 2025 - journals.lww.com
In the current review, we discuss the novelties for VEXAS, including pathogenic pathways,
epidemiological data, diagnostic criteria and algorithms, treatment options and …
epidemiological data, diagnostic criteria and algorithms, treatment options and …
VEXAS syndrome (vacuoles, E1 enzyme, X-linked, autoinflammatory, somatic): clinical review in a rapidly emerging field
L Phan, D Hammond, NR Wilson… - Leukemia & …, 2024 - Taylor & Francis
VEXAS syndrome is a recently described entity characterized by systemic inflammatory and
hematologic manifestations. The disease was first characterized by Beck et al. in 2020 in a …
hematologic manifestations. The disease was first characterized by Beck et al. in 2020 in a …
VEXAS syndrome diagnosis starting from ultrasound findings: a case report
T Rácz, S Burciu, T Torok, L Damian… - Medical …, 2024 - medultrason.ro
VEXAS syndrome is a recently described condition characterized by systemic inflammation,
predisposition to hematologic malignancy and a high rate of venous thrombosis. Here we …
predisposition to hematologic malignancy and a high rate of venous thrombosis. Here we …
VEXAS syndrome and thrombosis: findings of inflammation, hypercoagulability, and endothelial dysfunction
VEXAS (vacuoles, E1 enzyme, X-linked, autoinflammatory, somatic) syndrome is a novel
autoinflammatory syndrome due to a ubiquitin like modifier activating enzyme 1 (UBA1) …
autoinflammatory syndrome due to a ubiquitin like modifier activating enzyme 1 (UBA1) …
Aspects cliniques diagnostiques et thérapeutiques du syndrome VEXAS
P Breillat, B Terrier - Bulletin de l'Académie Nationale de Médecine, 2025 - Elsevier
Résumé VEXAS est un acronyme (vacuoles, enzyme E1, lié à l'X, auto-inflammatoire,
somatique) qui désigne un syndrome auto-inflammatoire décrit pour la première fois en …
somatique) qui désigne un syndrome auto-inflammatoire décrit pour la première fois en …
OP0243 EFFICACY AND SAFETY OF TARGETED THERAPIES IN VEXAS SYNDROME: RETROSPECTIVE STUDY FROM THE FRENVEX
J Hadjadj, Y Nguyen, D Mouloudj, R Bourguiba… - 2024 - ard.bmj.com
Background: VEXAS (Vacuoles, E1 enzyme, X-linked, Autoinflammatory, Somatic) syndrome
is an autoinflammatory disease of adults associated with somatic mutations in the UBA1 …
is an autoinflammatory disease of adults associated with somatic mutations in the UBA1 …
VEXAS syndrome: from a vascular perspective
AF Guédon - Blood, 2024 - ashpublications.org
The use of TKIs (first imatinib, followed by second-and third-generation TKIs) in combination
with conventional chemotherapy in children and young adults, or with reduced intensity in …
with conventional chemotherapy in children and young adults, or with reduced intensity in …
VEXAS-Syndrom: Paradigmenwechsel in der Differenzialdiagnose: Neues, eher häufiges autoentzündliches Krankheitsbild
K Thürmel - hautnah dermatologie, 2024 - Springer
Als Autoinflammation bezeichnet man unphysiologische entzünd liche Prozesse im Körper,
die nicht auf einer Immunantwort des adap tiven Immunsystems basieren, sondern …
die nicht auf einer Immunantwort des adap tiven Immunsystems basieren, sondern …