Lymphocyte depleting and modulating therapies for chronic lung allograft dysfunction
S Bos, P Pradère, H Beeckmans, A Zajacova… - Pharmacological …, 2023 - Elsevier
Chronic lung rejection, also called chronic lung allograft dysfunction (CLAD), remains the
major hurdle limiting long-term survival after lung transplantation, and limited therapeutic …
major hurdle limiting long-term survival after lung transplantation, and limited therapeutic …
COPA Syndrome from Diagnosis to Treatment: A Clinician's Guide
N Simchoni, TP Vogel… - Rheumatic Disease …, 2023 - rheumatic.theclinics.com
Methods Published articles and conference abstracts were identified through the literature
search for “COPA syndrome.” No relevant results returned for “autoimmune interstitial lung …
search for “COPA syndrome.” No relevant results returned for “autoimmune interstitial lung …
Lung transplantation under a Janus kinase inhibitor in three patients with SAVI syndrome
KR Berrada, A Belot, B Neven, C Ohlmann… - Journal of Clinical …, 2023 - Springer
Stimulator of interferon genes (STING)-associated vasculopathy with onset in infancy (SAVI)
is a very rare autoinflammatory disease related to STING1 mutation. SAVI is mainly …
is a very rare autoinflammatory disease related to STING1 mutation. SAVI is mainly …
Coatomer protein COPƐ, a novel NS1-interacting protein, promotes the replication of Porcine Parvovirus via attenuation of the production of type I interferon
S Chen, N Chen, B Miao, J Peng, X Zhang, C Chen… - Veterinary …, 2021 - Elsevier
Porcine Parvovirus (PPV) is a pathogen causing porcine reproductive disorders. Non-
structural protein NS1 appears diverse functions acting as a predominant regulator in …
structural protein NS1 appears diverse functions acting as a predominant regulator in …
Atteinte pulmonaire dans les maladies auto-inflammatoires
ML Frémond, L Berteloot, A Hadchouel - Revue des Maladies Respiratoires, 2024 - Elsevier
Résumé Les maladies auto-inflammatoires génétiques sont désormais un groupe de
maladies reconnu et en pleine expansion. L'atteinte pulmonaire historiquement associée …
maladies reconnu et en pleine expansion. L'atteinte pulmonaire historiquement associée …
[HTML][HTML] COPA Syndrome—From Pathogenesis to Treatment
Coatomer subunit α (COPA) syndrome is a mendelian autosomal dominant immune
dysregulation disease characterized by early onset lung disease in the form of diffuse …
dysregulation disease characterized by early onset lung disease in the form of diffuse …
Allograft dysfunction after lung transplantation for COPA syndrome: A case report and literature review
T Matsubayashi, M Yamamoto… - Modern …, 2022 - academic.oup.com
Coatomer subunit alpha (COPA) syndrome is an autoinflammatory disease with
autoimmune and autoinflammatory manifestations affecting lungs, joints, and kidneys. COPA …
autoimmune and autoinflammatory manifestations affecting lungs, joints, and kidneys. COPA …
Heterozygous mutations in the C-terminal domain of COPA underlie a complex autoinflammatory syndrome
S Delafontaine, A Iannuzzo, TM Bigley… - The Journal of …, 2024 - Am Soc Clin Investig
Mutations in the N-terminal WD40 domain of coatomer protein complex subunit α (COPA)
cause a type I interferonopathy, typically characterized by alveolar hemorrhage, arthritis, and …
cause a type I interferonopathy, typically characterized by alveolar hemorrhage, arthritis, and …