Mitochondrial fatty acid oxidation is an essential pathway for energy production, especially
during prolonged fasting and sub-maximal exercise. Long-chain fatty acids are the most …

Fatty acid oxidation disorders (FAODs) are inborn errors of metabolism due to disruption of
either mitochondrial β-oxidation or the fatty acid transport using the carnitine transport …

Mitochondrial fatty acid oxidation (FAO) plays a pivotal role in maintaining body energy
homoeostasis mainly during catabolic states. Oxidation of fatty acids requires approximately …

Carnitine plays essential roles in intermediary metabolism. In non-vegetarians, most of
carnitine sources (~ 75%) are obtained from diet whereas endogenous synthesis accounts …

Fatty acid oxidation disorders (FAOD) are a group of rare, autosomal recessive, metabolic
disorders caused by variants of the genes for the enzymes and proteins involved in the …

Fatty acid oxidation disorders (FAODs) are inborn errors of metabolism (IEMs) caused by
defects in the fatty acid (FA) mitochondrial β-oxidation. The most common FAODs are …

Malnutrition and sarcopenia are common in patients with chronic liver disease and are
associated with increased risk of decompensation, infections, wait-list mortality and poorer …

Mitochondrial fatty acid oxidation disorders (FAODs) are caused by defects in β-oxidation
enzymes, including very long-chain acyl-CoA dehydrogenase (VLCAD), trifunctional protein …

Background Observational reports suggest that supplementation that increases citric acid
cycle intermediates via anaplerosis may have therapeutic advantages over traditional …

NAFLD is the most common chronic liver disease worldwide, occurring in both obese and
lean patients. It can lead to life-threatening liver diseases and nonhepatic complications …