Sickle cell disease

JB Kunz, L Tagliaferri - Transfusion Medicine and Hemotherapy, 2024 - karger.com
Background: Sickle cell disease (SCD) is among the most frequent hereditary disorders
globally and its prevalence in Europe is increasing due to migration movements. Summary …

The efficacy of partial versus total splenectomy in the treatment of hereditary spherocytosis in children: a systematic review and meta-analysis

X Tang, J Xue, J Zhang, J Zhou - Pediatric Surgery International, 2024 - Springer
Objective To explore the comparative postoperative efficacy of partial splenectomy (PS) and
total splenectomy (TS) in the treatment of children with hereditary spherocytosis (HS) …

Morbidity and mortality of sickle cell disease patients is unaffected by splenectomy: evidence from three decades of follow-up in a high-income setting

VM Pinto, B Gianesin, FB Piel, F Longo… - …, 2022 - pmc.ncbi.nlm.nih.gov
Sickle cell disease (SCD) is a globally widespread hereditary red cell disorder characterized
by the production of pathological hemoglobin S (HbS). 1 Patients with SCD include …

[HTML][HTML] Current Status of Molecular Diagnosis of Hereditary Hemolytic Anemia in Korea

HW Chueh, YJ Shim, HL Jung, N Kim… - Journal of Korean …, 2024 - ncbi.nlm.nih.gov
Hereditary hemolytic anemia (HHA) is considered a group of rare hematological diseases in
Korea, primarily because of its unique ethnic characteristics and diagnostic challenges …

Partial splenectomy versus total splenectomy in sickle cell disease: A systematic review and meta-analysis

MR Roshdy, M Botros, A Mokhles… - Journal of Pediatric …, 2024 - Elsevier
Background Sickle cell disease (SCD) patients encounter various complications, such as
acute splenic sequestration crisis and hypersplenism that may require splenectomy. This …

Sickle Cell Disease

JBKL Tagliaferri - Transfus Med Hemother, 2024 - karger.com
Background: Sickle cell disease (SCD) is among the most frequent hereditary disorders
globally and its prevalence in Europe is increasing due to migration movements. Summary …

Partial splenectomy in children: Long-term reoperative outcomes☆

N Hafezi, KL Carpenter, CL Colgate, BW Gray… - Journal of Pediatric …, 2021 - Elsevier
Purpose Partial, or subtotal, splenectomy (PS) has become an accepted alternative to total
splenectomy (TS) for management of hematologic disorders in children, but little is known …

Postoperative complications and cost implications in sickle cell disease patients undergoing total hip arthroplasty: A national inpatient sample study

M Miskiewicz, R Madera, I Pesselev, J Gallagher… - Journal of …, 2025 - Elsevier
Background Sickle cell disease (SCD) is a genetic condition affecting approximately 5% of
the global population, with significant prevalence in sub-Saharan Africa and an estimated …

[HTML][HTML] Early splenectomy in sickle cell disease: another piece of the puzzle

R Colombatti, M Casale - Haematologica, 2023 - ncbi.nlm.nih.gov
Splenic involvement occurs very early in life in sickle cell anemia (SCA), which includes the
SS and Sβgenotypes, and later on in the SC and Sβ+ forms of sickle cell disease (SCD) …

Surgical Disorders of the Spleen

SJ Commander, ET Tracy, HE Rice - Fundamentals of Pediatric Surgery, 2022 - Springer
Splenectomy is often considered for children with various benign and malignant conditions.
Total splenectomy (TS) or partial splenectomy (PS) can safely be performed in children with …