Pleuroparenchymal fibroelastosis (PPFE) is an unusual pulmonary disease with unique
clinical, radiological, and pathological characteristics. Designated a rare idiopathic …

Background Physicians have few opportunities to perform surgical lung biopsy (SLB) to
diagnose idiopathic pleuroparenchymal fibroelastosis (IPPFE). Therefore, diagnostic criteria …

Pleuroparenchymal fibroelastosis (PPFE) is a rare pulmonary fibrosis that is clinically
characterized by upperlobe predominant fibrosis. PPFE is a slowly progressive disorder and …

BACKGROUND Pleuroparenchymal fibroelastosis (PPFE) is a rare form of interstitial
pneumonia and sometimes coexists with a histologic usual interstitial pneumonia (UIP) …

Interstitial lung diseases (ILDs) that are known as diffuse parenchymal lung diseases
(DPLDs) lead to the damage of alveolar epithelium and lung parenchyma, culminating in …

Pleuroparenchymal fibroelastosis : Current Opinion in Pulmonary Medicine
Pleuroparenchymal fibroelastosis : Current Opinion in Pulmonary Medicine Log in or …

The world of rare interstitial lung diseases (ILDs) is diverse and complex. Diagnosis and
therapy usually pose challenges. This review describes a selection of rare and ultrarare …

Objective. Idiopathic pleuroparenchymal fibroelastosis (IPPFE) is a rare disease
characterized by predominant upper lobe pulmonary fibrosis of unknown etiology. However …

BACKGROUND Pleuroparenchymal fibroelastosis (PPFE) has been described in
hypersensitivity pneumonitis (HP) yet its functional implications are unclear. Combined …

Pleuroparenchymal fibroelastosis (PPFE) is a distinct pattern of pulmonary fibrosis which
often runs a rapidly progressive course with a poor prognosis, and it is likely to be …