Objective To compare performance after cochlear implantation in children with mutations in
connexin (Cx) 26 (GJB2) or Cx30 (GJB6) and children with deafness of unknown etiology …

Conclusions: Implanted children with GJB2 mutations tended to achieve better functional
outcomes than the two control groups, although clear-cut significance was not always …

Background: Cochlear implants (CI) for the rehabilitation of patients with profound or total
bilateral sensorineural hypoacusis represent the initial use of electrical fields to provide …

Background: There is significant variability in the degree of intelligibility, or clarity, of
children's speech after cochlear implantation. GJB2 gene-related deafness may be a factor …

Conclusion: There were no apparent differences in speech performance after cochlear
implantation between patients with biallelic GJB2 and/or GJB6 mutations and those with …

Background: Preliminary data suggest pathologic changes due to GJB2 mutations do not
affect the spiral ganglion cells, which are stimulated by the cochlear implant. The survival of …

This study addressed the question of whether a hearing loss caused by mutations in the
connexin 26 gene had a significant effect on language and speech perception outcomes in …

Abstract Objectives/Hypothesis: Mutations in GJB2 are a common cause of congenital
sensorineural hearing loss. Many children with these mutations receive cochlear implants …

Abstract Objectives/Hypothesis It has been hypothesized that etiology of hearing loss may
serve as an independent variable in performance after cochlear implantation. To test this …

Background Hitherto more than hundred genes and gene loci for non-syndromic or
syndromic deafness have been identified. Mutations in the connexin 26 gene (GJB2) …